Aggressive angiomyxoma of vulva: a rare and interesting entity

We report a case of 44-year-old female with aggressive angiomyxoma arising from right labia majora. The patient presented gradually enlarging vulvar mass and was treatment included wide local excision the R0 resection. Pre operative final histopathology consistent features angiomyxoma. Angiomyxoma is rare, benign, locally infiltrative mesenchymal tumor that occurs in females at reproductive age. Repeated recurrence invasive characteristics makes it important to be considered as part differential diagnosis especially cases pelvic females.